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Allergy, Asthma & Clinical Immunology
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Table 1
Laboratory findings in hereditary angioedema
From:
Canadian hereditary angioedema guideline
C4
C1-INHAntigen
C1INH Function
HAE - 1
↓
↓
↓
HAE - 2
↓
Normal or
↑
↓
HAE - nC1INH
-FXII mutation
Normal
Normal
Normal
-UnknownCause
Normal
Normal
Normal
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