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Table 1 Laboratory findings in hereditary angioedema

From: Canadian hereditary angioedema guideline

 

C4

C1-INHAntigen

C1INH Function

HAE - 1

↓

↓

↓

HAE - 2

↓

Normal or

↑

↓

HAE - nC1INH

   

 -FXII mutation

Normal

Normal

Normal

 -UnknownCause

Normal

Normal

Normal

  1. References [9, 10].