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Table 1 Treatments in hereditary angioedema with normal C1-INH (HAE type III) as reported up to now

From: Diagnosis and treatment of hereditary angioedema with normal C1 inhibitor

  Treatment effective (no. of patients; [reference]) Treatment not effective (no. of patients; [reference])
Acute attacks   
C1-INH concentrate 6 [14] 4 [1]
   1 [14]
Icatibant 3 [37] 0
Corticosteroids 0 23 [1]
   1 [7]
   1 [22]
Antihistamines 0 23 [1]
   1 [7]
   1 [21]
   1 [22]
Adrenalin 0 1 [21]
Prophylaxis   
Androgens 2 [1] 0
  1 [3]  
  1 [38]  
Tranexamic acid 1 [10] 2 [1]
  1 [14] 1 [37]
Progesterone 1 [5] 0
  1 [10]  
  8 [14]