From: Urticaria and angioedema
Age of onset | Family history | Complement levels | ||||
---|---|---|---|---|---|---|
C1q | C4 | C1 inh level | C1 inh function | |||
HAE
Type 1 Type 2 | Early | Yes* |
Normal Normal |
Low Low |
Low Normal/elevated |
Low Low |
AAE | Late | No | Low | Low | Normal or low | Low |