Characteristic | Patients with HAE type I or II | |
---|---|---|
UK (N = 73) | Non-UK (N = 579) | |
Age at extract, years | ||
 Mean (SD) | 42.9 (14.7)a | 45.1 (15.2)b |
 Median (range) | 42.2 (18–82)a | 43.3 (6–86)b |
Gender, n (%) | ||
 Male | 29 (39.7) | 235 (40.6) |
 Female | 44 (60.3) | 344 (59.4) |
Age at first symptoms, years | ||
 Mean (SD) | 11.3 (9.5)c | 14.1 (11.2)d |
 Median (IQR) | 10.0 (5.0, 16.0)c | 13.0 (6.0, 19.0)d |
Age at diagnosis, years | ||
 Mean (SD) | 21.5 (12.7)e | 24.6 (15.9)f |
 Median (IQR) | 18.9 (12.6, 30.0)e | 21.0 (13.2, 34.2)f |
Delay between first symptoms and diagnosis, years | ||
 Mean (SD) | 9.5 (13.9)c | 10.5 (13.6)g |
 Median (IQR) | 6.2 (0.0, 17.5)c | 5.9 (0.4, 17.6)g |
Employment status, n (%)h | ||
 Employee | 46 (63.0) | 218 (52.0) |
 Self-employed | 7 (9.6) | 15 (3.6) |
 Homemaker | 3 (4.1) | 20 (4.8) |
 Leave of absence/sabbatical | 1 (1.4) | 2 (0.5) |
 Pre-school | 0 | 4 (1.0) |
 Retired | 3 (4.1) | 42 (10.0) |
 Student | 8 (11.0) | 53 (12.6) |
 Unemployed | 4 (5.5) | 34 (8.1) |
 Other/unknown | 4 (5.5) | 43 (10.3) |