From: Preliminary study on chronic granulomatous disease in Sri Lanka
Country/region | Number of patients | Gender | Consangui-nity | CGD subtype | Deaths | ||
---|---|---|---|---|---|---|---|
Male | Female | X-linked | AR | ||||
Sri Lanka | 12 | 10 | 2 | 6 (46%) | 6 (75%) | 2 (25%) | 4 (38.4%) |
India [2] | 17 | 15 | 2 | 2 (11.7%) | 7 (41%) | 10 (59%) | 6 (35%) |
Iran [12] | 41 | 29 | 12 | 23 (56.1%) | 5 (12.2%) | ||
Turkey [3] | 89 | 64 | 25 | 42 (57.5%) | 34 (38.2%) | 55 (61.8%) | 9 (10.1%) |
China [14] | 48 | 44 | 4 | 0 | 36 (75%) | 3 (6%) | 11 (22%) |
Latin America [10] | 71 | 58 | 13 | – | 53 (74.6%) | 18 (25.3%) | – |
Europe [1] | 429 | 351 | 78 | – | 290 (67%) | 139 (33%) | 84 (20%) |
USA [11] | 368 | 316 | 52 | – | 259 (70%) | 81 (22%) | 65 (17.6%) |