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Table 2 Flu/Mel/TBI 3 Gy conditioning HCT for XLP1 in Japan

From: Hematopoietic cell transplantation for asymptomatic X-linked lymphoproliferative syndrome type 1

Age Symptoms Donor
Source
HLA matching GVHD prophylaxis aGVHD cGVHD Outcome References
3 years HLH, hypo-γ Unrelated
BM
4/6 Tacrolimus/sMTX Grade I None Alive (8 years) [5]
7 years Hypo-γ Unrelated
BM
6/6 Tacrolimus/sMTX None Extensive Alive (4 years) [5]
15 years HLH, ML, hypo-γ Unrelated
BM
6/6 Tacrolimus/sMTX None None Alive (3 years) [5]
20 months Asymptomatic Unrelated
BM
8/8 Tacrolimus/sMTX Grade I None Alive (2 years) Our patient
  1. HLH hemophagocytic lymphohistiocytosis, hypo-γ hypo gammaglobulinemia
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