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Table 1 Laboratory findings in hereditary angioedema [9,10,11]

From: The International/Canadian Hereditary Angioedema Guideline

Function

C4

C1-INH antigen

C1-INH

HAE-1

↓

↓

↓

HAE-2

↓

normal or ↑

↓

HAE-nC1INH variants

 coagulation factor XII

 angiopoietin-1

 plasminogen

 unknown

normal

normal

normal