From: The International/Canadian Hereditary Angioedema Guideline
Function | C4 | C1-INH antigen | C1-INH |
---|---|---|---|
HAE-1 | ↓ | ↓ | ↓ |
HAE-2 | ↓ | normal or ↑ | ↓ |
HAE-nC1INH variants  coagulation factor XII  angiopoietin-1  plasminogen  unknown | normal | normal | normal |