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Table 1 Number of individual published mentions of HAE-C1INH and autoimmune disease comorbidity

From: Co-occurrence between C1 esterase inhibitor deficiency and autoimmune disease: a systematic literature review

Autoimmune disease

Number of HAE comorbid mentions

 Lupus or lupus-like diseases

52

  Systemic lupus erythematosus

30

  Lupus (unspecified)

7

  Discoid lupus

8

  Lupus-like disease

4

  Cutaneous lupus

2

  Drug-induced lupus

1

 Thyroid disease

21

  Hypothyroidism

10

  Thyroiditis

5

  Anti-thyroid antibodies

3

  Hashimotos

2

  Unspecified

1

 Glomerulonephritis

16

 Rheumatoid arthritis

11

 Crohn’s disease

8

 Various autoantibodies

8

 Sjogren’s syndrome

7

 Celiac disease

7

 Psoriasis

3

 Antiphospholipid syndrome

3

 Autoimmune hemolytic anemia/anemia

3

 General/unspecified autoimmune disease

2

 Psoriatic arthritis

2

 Systemic sclerosis

2

 Mixed connective tissue disease

2

 Raynauds syndrome

2

 Urticarial vasculitis

1

 Sicca syndrome

1

 Lipodystrophy

1

 Alopecia

1

 Multiple-sclerosis-like syndrome

1

 Ulcerative colitis

1

  1. C1-INH C1 esterase inhibitor, HAE hereditary angioedema