Skip to main content

Table 2 Number of individual published mentions of HAE-C1INH and AD comorbidity grouped by MedDRA v21.0 high level terms

From: Co-occurrence between C1 esterase inhibitor deficiency and autoimmune disease: a systematic literature review

High level MedDRA term

Number of HAE comorbid AD mentions

 Lupus erythematosus and associated conditions

52

  Systemic lupus erythematosus

30

  Lupus

7

  Discoid lupus

8

  Lupus-like disease

4

  Cutaneous lupus

2

  Drug-induced lupus

1

 Endocrine autoimmune disorders

21

  Thyroid diseases

21

 Glomerulonephritis and nephrotic syndrome

16

  Glomerulonephritis

16

 Gastrointestinal inflammatory conditions

16

  Crohn’s disease

8

  Celiac disease

7

  Ulcerative colitis

1

 Rheumatoid arthritis and associated conditions

11

  Rheumatoid arthritis

11

 Eye, salivary gland and connective tissue disorders

10

  Sjogren’s syndrome

7

  Sicca syndrome

1

  Mixed connective tissue disease

2

 Immune and associated conditions not elsewhere classified

5

  Psoriasis

3

  Psoriatic arthritis

2

  1. Groups with ≥ 5 mentions are shown
  2. AD autoimmune disease, C1-INH C1 esterase inhibitor, HAE hereditary angioedema, MedDRA Medical Dictionary for Regulatory Activities