AI condition | Number (%) of patients | ||
---|---|---|---|
HAE index medication | Total (N = 589) | ||
Cinryze/Berinert | Firazyr/Kalbitor | ||
Any AI condition | 42 (7.13) | 34 (5.77) | 76 (12.9) |
Lupus erythematosus | 12 (2.04) | 7 (1.19) | 19 (3.23) |
Alopecia | 6 (1.02) | 7 (1.19) | 13 (2.21) |
Rheumatoid arthritis | 9 (1.53) | 3 (0.51) | 12 (2.04) |
Sicca syndrome | 6 (1.02) | 6 (1.02) | 12 (2.04) |
Connective tissue disorders | 5 (0.85) | 7 (1.19) | 12 (2.04) |
Crohn disease | 3 (0.51) | 6 (1.02) | 9 (1.53) |
Celiac disease | 6 (1.02) | 2 (0.34) | 8 (1.36) |
Raynaud’s disease | 4 (0.68) | 4 (0.68) | 8 (1.36) |
Thyroiditis | 3 (0.51) | 3 (0.51) | 6 (1.02) |
Psoriasis | 2 (0.34) | 4 (0.68) | 6 (1.02) |
Antiphospholipid syndrome | 3 (0.51) | 2 (0.34) | 5 (0.85) |
Rheumatism | 2 (0.34) | – | 2 (0.34) |
Systemic sclerosis (scleroderma) | – | 2 (0.34) | 2 (0.34) |
Ulcerative colitis | – | 2 (0.34) | 2 (0.34) |
Nephritic syndrome | 1 (0.17) | – | 1 (0.17) |