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Table 1 Autoimmune conditions present in at least 1 visit

From: Hereditary angioedema C1-esterase inhibitor replacement therapy and coexisting autoimmune disorders: findings from a claims database

AI condition

Number (%) of patients

HAE index medication

Total (N = 589)

Cinryze/Berinert

Firazyr/Kalbitor

Any AI condition

42 (7.13)

34 (5.77)

76 (12.9)

Lupus erythematosus

12 (2.04)

7 (1.19)

19 (3.23)

Alopecia

6 (1.02)

7 (1.19)

13 (2.21)

Rheumatoid arthritis

9 (1.53)

3 (0.51)

12 (2.04)

Sicca syndrome

6 (1.02)

6 (1.02)

12 (2.04)

Connective tissue disorders

5 (0.85)

7 (1.19)

12 (2.04)

Crohn disease

3 (0.51)

6 (1.02)

9 (1.53)

Celiac disease

6 (1.02)

2 (0.34)

8 (1.36)

Raynaud’s disease

4 (0.68)

4 (0.68)

8 (1.36)

Thyroiditis

3 (0.51)

3 (0.51)

6 (1.02)

Psoriasis

2 (0.34)

4 (0.68)

6 (1.02)

Antiphospholipid syndrome

3 (0.51)

2 (0.34)

5 (0.85)

Rheumatism

2 (0.34)

–

2 (0.34)

Systemic sclerosis (scleroderma)

–

2 (0.34)

2 (0.34)

Ulcerative colitis

–

2 (0.34)

2 (0.34)

Nephritic syndrome

1 (0.17)

–

1 (0.17)

  1. AI autoimmune, HAE hereditary angioedema, N total number of patients with HAE due to C1-inhibitor deficiency