Criteria | n (%) |
---|---|
Non complicated patients | 21 (31) |
Cytopenia | |
Autoimmune hemolytic anemia | 3 (4) |
Neutropenia | 3 (4) |
Immune thrombocytopenia | 12 (18) |
Autoimmunity | |
Yes | 30 (44) |
Granulomatosis | |
Yes | 12 (18) |
Granulomatous and lymphocytic interstitial lung disease | 6 (9) |
Granulomatosis in only 1 site | 3 (4) |
Granulomatosis in > 1 site | 9 (13) |
CVID-associated enteropathy | |
Yes | 11 (16) |
Helicobacter pylori positivity | 18 (26) |
Allergies | |
Overall | 15 (22) |
Drugs | 12 (18) |
Splenectomy | 6 (9) |
Therapy | |
20% SCIg replacement therapy | 28 (42) |
Facilitated SCIg replacement therapy | 17 (25) |
IVIg replacement therapy | 26 (38) |