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Table 2 Clinical features and kind of treatment at last follow-up visit in 67 common variable immunodeficiency patients

From: Incidence of malignancy in patients with common variable immunodeficiency according to therapeutic delay: an Italian retrospective, monocentric cohort study

Criteria

n (%)

Non complicated patients

21 (31)

Cytopenia

 

 Autoimmune hemolytic anemia 

3 (4)

 Neutropenia

3 (4)

 Immune thrombocytopenia

12 (18)

Autoimmunity

 

 Yes

30 (44)

Granulomatosis

 

 Yes

12 (18)

Granulomatous and lymphocytic interstitial lung disease

6 (9)

Granulomatosis in only 1 site

3 (4)

Granulomatosis in > 1 site

9 (13)

CVID-associated enteropathy

 

 Yes

11 (16)

Helicobacter pylori positivity

18 (26)

Allergies

 

 Overall

15 (22)

 Drugs

12 (18)

 Splenectomy

6 (9)

Therapy

 

 20% SCIg replacement therapy

28 (42)

 Facilitated SCIg replacement therapy

17 (25)

 IVIg replacement therapy

26 (38)

  1. CVID: Common variable immunodeficiency; IVIg: intravenous immunoglobulin; SCIg: subcutaneous immunoglobulin