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Table 3 Lymphocyte subsets results in flow cytometry

From: X-linked SCID with a rare mutation

Normal range

6 years old

5 years old

4 years old

Test

65–88%

(1400–3700)

64

(4000)

60 (4600/µl)

CD3%

Number (cells//µl)

26–62%

700–2200

17.5% (1093/µl)

17% (2450/µl)

19% (1459/µl)

CD4%

14–44%

490–1300

34.5% (2156/µl)

31% (3930/µl)

27% (2073/µl)

CD8%

0.9–2.9

0.5

0.5

0.7

CD4/CD8

 

1.98% (borderline) Absolute count = 125

TCRαβ + CD4-CD8-%

2–27%

390–1400

13.3% (8312/µl)

23% (2900/µl)

26.2% (2012/µl)

CD19%

14%

390–1400

13.5% (843/µl)

25% (3155/µl)

23.7% (1820/µl)

CD20%

9%

21% (16 + 56 +) (1312/µl)

19% (2397/µl)

26.6% (2042/µl)

CD16%

12%

24% (1500/µl)

21% (2650/µl)

26.2% (2012/µl)

CD56%

32–76%

81.5%

Naïve B cell

1.2–10%

2.84%

Marginal zone like B cells

2–16%

2.78%

Switched memory B cells

1–12%

12%

Transitional B cells

1–4%

4%

CD21 B cell

0.2–4%

0.4%

Plasma cell

32–71%

23.6%

Naïve CD4 T cell

10–39%

5.1%

Central memory CD4 T cell

9–39%

45.5%

Effector memory CD4 T cell

19–76%

22.5%

Naïve CD8 T cell

0.3–9%

0.06%

Central memory CD8 T cell

6–33%

36.3%

Effector memory CD8 T cell