Characteristic | Spain n = 119 | Other Countriesa n = 907 |
---|---|---|
Sex, n (%) | ||
Female | 64 (53.8) | 548 (60.4) |
Male | 55 (46.2) | 359 (39.6) |
HAE type, n (%) | ||
HAE-1 | 114 (95.8) | 838 (92.4) |
HAE-2 | 5 (4.2) | 69 (7.6) |
Median (IQR) age at first symptoms, y | 15.0 (5.0–20.0) | 12.0 (5.0–18.0) |
Median (IQR) age at diagnosis, y | 22.3 (13.6–36.0) | 20.5 (12.6–32.9) |
Median (IQR) time to diagnosis, yb | 6.4 (1.0–18.3) | 5.4 (0.2–17.0) |
Median (IQR) age at enrollment, y | 39.3 (27.2–50.4) | 39.0 (27.5–51.8) |
Median (IQR) age at data extract, y | 45.0 (34.0–56.0) | 44.0 (32.0–57.0) |
Median (IQR) duration of follow-up in IOS, y | 5.6 (1.2–7.0) | 2.4 (0.4–4.9) |