Table 1 Consensus diagnostic criteria for IgG4-RD
IgG4 related disease diagnostic criteria | |
|---|---|
Criteria I | Organ enlargement, mass or nodal disease, or organ dysfunction |
Criteria II | A serum IgG4 concentration of > 135 mg/dL |
Criteria III | Histopathological findings characteristic of IgG4-RD: IgG4+/IgG+cell ratio> 40% and > 10 IgG4+plasma cells per high-power field |
Igg4 related disease diagnostic algorithm | |
|---|---|
Diagnostic criteria met | Diagnosis probability |
Criteria I, II, III | Definite |
Criteria I, III | Probable |
Criteria I, II | Possible |
No criteria met | Negative |