Table 1 Laboratory data around the time of presentation

Blood test

Normal range

Normal range

WBC, /μL

4700–8700

anti-nuclear Ab

1: 80

 < 40

Stab, %

0.0–13.0

(staining patterns)

nucleolar, speckled

Seg, %

38.0–58.9

anti-ds-DNA Ab, IU/mL

 < 5.0

0.0–12.0

Eos, %

0.2–6.8

anti-Smith Ab, U/mL

 < 3.0

0.0–10.0

Baso, %

0.0–1.0

anti-RNP Ab, U/mL

14.2

0.0–10.0

Mono, %

2.3–7.7

anti-SS-A Ab, U/mL

48,550.0

0.0–10.0

Lym, %

26.0–46.6

anti-SS-B Ab, U/mL

 < 3.0

0.0–10.0

RBC, × 10^4/μL

370–490

Direct Coombs

( +)

Hb, g/dL

11.0–15.0

Indirect Coombs

(-)

Hct, %

35.0–45.0

anti-platelet Ab

(-)

Plt, × 10^4/μL

15.0–35.0

PA-IgG, ng/10⁷cells

42.7

 < 46

Lac, ratio

1.13

0.00–1.30

CRP, mg/dL

0.00–0.20

CL-IgG, U/mL

 < 8.0

0.0–10.0

TP, g/dL

6.5–8.2

CLβ2-GP1 Ab, U/mL

 < 0.7

0.0–3.5

Alb, g/dL

3.5–5.5

BUN, mg/dL

7.0–20.0

β-D glucan, pg/mL

 < 6.0

0.0–11.0

Cre, mg/dL

0.50–1.00

Procalcitonin, ng/mL

0.05

0.00–0.49

GOT, IU/L

13–30

HBs-Ag

(-)

GPT, IU/L

7–23

HCV-Ab

(-)

ALP, IU/L

106–322

EBV-VCA-IgG

( +)

γ-GTP, IU/L

9–32

EBV-VCA-IgM

(-)

LDH, IU/L

124–222

EBV-EA-IgG

(-)

Amylase, U/L

44–132

EBV-EA-IgM

(-)

Ferritin, ng/mL

6.0–138

EBNA-Ab

( +)

sIL-2R, U/mL

121–613

CMV-IgG

( +)

IgA, mg/dL

114–435

CMV-IgM

(-)

IgG, mg/dL

870–1700

CMV Ag (10, 11)

(-)

IgM, mg/dL

46–260

Parvovirus B19-IgM

(-)

C3, mg/dL

68–114

C4, mg/dL

12–33

Urinalysis

CH50, U/mL

30–50

Protein

( ±)

C1 inhibitor activity, %

70–130

Protein, g/gCr

0.21

RBC

(1 +)

C1 inhibitor levels, mg/dL

21–39

NAG, U/L

15.5

0.7–11.2

β2-microglobulin, µg/L

3259

0–250

PT-INR

0.85–1.15

APTT, sec

27.0–47.0

Fibrinogen, mg/dL

200–400

D-dimer, μg/mL

0.0–1.0