From: Severe congenital neutropenia due to G6PC3 deficiency: early and delayed phenotype of a patient
3 days after G-CSF treatment | 2 weeks after G-CSF treatment | Age-related Ref. values | |||
---|---|---|---|---|---|
Absolute number | Percentage | Absolute number | Percentage | ||
WBC | 1.94 (103/uL) | 9.25 (103/uL) | 4.0–10.3 (103/uL) | ||
RBC | 3.80 (106/uL) | 4.96 (106/uL) | 4.4–5.6 (106/uL) | ||
HGB | 10.2 (g/dL) | 11.9 (g/dL) | 12.3–16.3 (g/dL) | ||
HCT | 31.0 (%) | 34.8 (%) | 35.4–43.4 (%) | ||
MCV | 81.6 (fL) | 70.2 (fL) | 76.9–87.2 (fL) | ||
MCH | 26.8 (pg) | 24 (pg) | 25.8–30.0 (pg) | ||
MCHC | 32.9 (g/dL) | 34.2 (g/dL) | 32.3–35.9 (g/dL) | ||
PLT | 54 (103/uL) | 193 (103/uL) | 216–469 (103/uL) | ||
RDW-SD | 56.6 (fL) | 33.5 (fL) | |||
RDW-CV | 19.7 (%) | 13.4 (%) | 11.9–14.3 (%) | ||
NEUT | 1.03 (103/uL) | 53.1 (%) | 1.52 (103/uL) | 16.5 (%) | 32.3–64.1 (%) |
LYMPH | 0.62 (103/uL) | 32.0 (%) | 6.42 (103/uL) | 69.5 (%) | 26.1–57.5 (%) |
MONO | 0.28 (103/uL) | 14.4 (%) | 1.14 (103/uL) | 12.3 (%) | 3.9–10 (%) |
EO | 0.00 (103/uL) | 0.0 (%) | 0.17 (103/uL) | 1.8 (%) | 0.4–7.5 (%) |
Baso | 0.01 (103/uL) | 0.5 (%) | 0.0 (103/uL) | 0.0 (%) | 0.1–1.0 (%) |
IgM | 156 (37–286) | ||||
IgG | 2881 (639–1349) | ||||
IgA | 140 (42–295) |