COMPACT study C1-INH(SC) 60 IU/kg (N = 45) | CHANGE study C1-INH(IV) 1000 U (N = 22) | |
---|---|---|
Age, y | ||
Mean (SD) | 36.8 (14.9) | 38.1 (17.2) |
Median (range) | 35.0 (14, 72) | 38.5 (9, 73) |
Gender, n (%) | ||
Female | 32 (71.1) | 20 (90.9) |
Male | 13 (28.9) | 2 (9.1) |
Race, n (%) | ||
White | 44 (97.8) | 21 (95.5) |
Black/African-American | 1 (2.2) | 1 (4.5) |
Asian | 0 | 0 |
Other | 0 | 0 |
Weight, kg | ||
Mean (SD) | 80.2 (24.6) | 73.4 (18.9) |
Median (range) | 78.0 (43.0, 156.8) | 69.3 (37.6, 113.9) |
HAE type, n (%) | ||
Type 1 | 37 (82.2) | 18 (81.8) |
Type 2 | 8 (17.8) | 4 (18.2) |