From: Chronic idiopathic systemic capillary leak syndrome: a case report
Agent | Dose | Duration | Response |
---|---|---|---|
Methyl-prednisone | 500Â mg/day | Several doses | No |
IVIG | 2Â gm/kg | Several doses followed by monthly for 6Â months | No |
Intravenous theophylline | 5Â mg/kg followed by 0.4Â mg/kg/h | 2Â days | No |
Terbutaline | 5Â mg three times/day | 14Â days | No |
Bevacizumab | 5Â mg/kg | 2 doses 2Â weeks apart | No |
Intravenous methylene blue | 2Â mg/kg | One dose | No |
Thalidomide | 200Â mg daily | 4Â months | No |